5 Cases Report Of Primary Intestinal Lymphangiectasia

Intestinal lymphangiectasia(IL)is a disease characterized by dilated lymaphatic vassles in the intestinal wall and small bowel mesentery which induce loss of protein and lymphocytes into bowel lumen,induce to hypoproteinemia,diarrhea and lymphocytopenia.It's separate to primarily and secondary.Until now,there were a few case report about this disease.There are 5 cases report and discussion about it's diagnosis and treatment.ObjectiveTo improve the comprehesion of Intestinal lymphangiectasia(IL)especially Primary Intestinal lymphangiectasia(PIL).Clinical Materials and Methods5 cases of PIL treated in our hospital from 1996-2007 were studied and the clinical information,laboratory data,radiological images,endoscopic,pathological findings and prognosis were analyzed.1.Among the 5 patients,2 were male while 3 were female,the age distributed from 22-71,and the mean age in this series of 5 patients was 43.6 years.2.5 patients presented with abdominal distention and 4patients with edema, 3cases with ascites,2 cases with iarrhea,1 case with Dark stools.3.All patients presented with peripheral blood lymphocyte;peripheral-blood lymphocyte degrade,Hypoproteinemia,2 case with IgG loss.4.1 patient with superior mesenteric angiography:abnormal vascular pool supplied by arteria ileocolica,peripheral vessel were intensive and fuzzy, GIST? 2 patients with intestine visualization:dilat enteric cavity,thickening and disord mucosae,filling defect.5.1 patient with capsule endoscopy:small intestine paliform lymphangiectasis, dilat lymphatic vessel and blood capillary were found.6.2 patients diagnosed as IL before operations research,1 patient diagnosed as GIST,2 case acatalepsia,1 of 5 patients acatalepsia after twice operations research.5 patients used operations research,2 patients with chyliform ascites, 3 patients with broaden lymphangion,,3 patients with incrassate bowel.All diagnosis received pathematology support.7.5 patients treated by surgical intervention,4 patients were cut the dilat bowel,1 patient with abdominal cavity and left femoral vein by-pass,then albumen infusion,diuresis,diet instruction,and other support therapy were given.8.Follow-up visit:1-4 years,no recurrence.Conclusion For patient with edema,abdominal distention or ascites,when lab test reveal hypoproteinemia or hypophocytopenia,IL should be suspected.The mainstay of treatment for IL include correcting the underlying disease responsible for the IL,MCT supplemented,surgical treatment also can be considered in certain patients.