Progress In Diagnosis And Treatment Of Hemophagocytic Syndrome

Hemophagocytic syndrome(hemophagocytic lymphohistiocytosis,HLH)represent a severe hyperinflammatory condition with the cardinal symptoms prolonged fever,cytopenias,hepatosplenomegaly.Biochemical markers include elevated ferritin and triglycerides,and low fibrinogen.Depending on the etiology,HLH can be divided into genetic(primary)and acquired(secondary)forms.HLH is a rare fatal disease with insidious onset and complicated clinical manifestations,often accompanied by multiple organ damage.It is a dangerous disease with rapid progress and high mortality.It often dies due to multiple organ failure.There is no effectual treatment for HLH currently.The therapeutic methods for HPS shouldbe further studied...