The Clinical Features Of 83 Cases Of Pediatric Cardiomyopathy Were Analysis And Literature Review

Objective: To explore the clinical characteristics of pediatric cardiomyopathy and improve the diagnosis and treatment of children cardiomyopathy.Methods: 83 cases of cardiomyopathy were retrospectively analyzed,including family history,clinical manifestation,auxiliary examination and diagnosis and treatment,and related literature review.Results: In the majority with young age children pediatric cardiomyopathy onset age,clinical manifestations,elastic fibrous hyperplasia with higher incidence of endocardial boy 27 cases,25 cases of the girls,the onset of age-February 6,8 months average onset age,0-6 months among 20 cases(38.5%),6 months,1 year old among 19 cases(36.5%),more than 1 years old among 13 cases(25.0%).Hospitalization is usually associated with respiratory tract infection(mostly pulmonary infection)and(or)cardiac dysfunction,and hospitalization at the time of diagnosis.This disease has a high fatality rate and long course of disease.It is necessary to take drug therapy for a long time.After discharge,we continued to take the drug therapy regularly,followed by a regular follow-up of 46 patients in our pediatric outpatient department,with a follow-up rate of 88.5%(46/52),6 cases lost,and the loss rate of 11.5%(6/52).The history of HCM was found in 3 patients with family history and 2 cases of DCM.Children with DCM onset hidden,slow,with weakness,fatigue,edema,and shortness of breath during hospitalization,overworked disorder gradually improved in 16 cases,improvement is not obvious in 1 case,aggravating readmission in 1 case,aggravating reasons for upper respiratory tract infection,stop,etc.The mortality rate of dilated cardiomyopathy was 0.55% during hospitalization,and most of the patients died of severe heart failure and arrhythmia,among which arrhythmias were most common in atrial premature beats and ventricular premature beats.The clinical manifestations of the cardiomyopathy has obvious difference,the person that weigh can have obvious weakness,shortness of breath,dyspnea,edema,syncope,and even death,light person but no clinical manifestation,found only in physical examination.The treatment plan is mainly to prevent heart failure,to correct arrhythmias,thrombolysis,and to choose the immune globulin and other comprehensive treatment.Endocardial elastic fibrosis ultrasound can be seen in the left ventricular endometrium thickening,the heart cavity is enlarged,and the ventricular wall motion is weakened.Dilated cardiomyopathy echocardiogram left ventricular ejection fraction(EF)and shortened score(SF)decreased,ventricular wall motion was decreased,and the cardiothoracic cavity was enlarged.Myocardial densification of incomplete echocardiography is characterized by decreased cardiac systolic and diastolic function,intimal echo enhancement,enlarged left ventricular cavity and relative valve closure.Hypertrophic cardiomyopathy(echocardiography)shows asymmetrical ventricular hypertrophy,and the clinical manifestations of children with different LVEF can be reduced.In addition echocardiography can also be seen with pericardial effusion.UCG examination of LVEF in children with restricted cardiomyopathy was mostly normal.About 46.1% of children with cardiomyopathy of UCG check under the aortic pressure difference greater than 30 MMHG(1 MMHG=0.133 KPa),tachycardia cardiomyopathy patients to control arrhythmia,heart failure in clinical manifestations and UCG heart function index of 18 ~ 36 d back to normal.The incidence of ecg was 69.78%,and the incidence of arrhythmia was 36.26%,which was mainly caused by premature beats and tachycardia.The common characteristic of EFE children was the change of ST segment.The electrocardiogram of DCM can be characterized by various types of arrhythmias,which are more common with ventricular tachycardia,T wave inversion,atrioventricular block,and a few pathological Q waves.Patients with long illness are often serious,extremely difficult to control,and life threatening.Conclusion: The clinical manifestation of patients with cardiomyopathy is very different,which can range from no obvious clinical symptoms to severe heart failure and arrhythmia.Some of the children had family history,and the age,clinical manifestation and laboratory examination of children with cardiomyopathy in the same department were significantly different.At present,there is no special treatment method for children cardiomyopathy,which aims to relieve clinical symptoms and improve the quality of life.