Microscopic polyangiitis is a kind of necrotizing vasculitis,whichinvolves multiple systems and organs. The lung is an important organinvolved, and microscopic polyangiitis with pulmonary fibrosis is a factorthat reflects a patient’s severity of the condition and prognosis. In order toraise awareness of microscopic polyangiitis with pulmonary fibrosis,reducemisdiagnosis and improve patient outcomes,this review focuses onmicroscopic polyangiitis and pulmonary fibrosis. |